Unmasking Postsurgical Ectasia in Paediatric Patient

Background

Post-surgical ectasia is a complication in which a cornea that has undergone a refractive surgical procedure becomes progressively irregular and thinned leading to protrusion and undesirable visual disturbances such as blur and higher order aberrations. When screening a candidate for LASIK, many factors must be considered to reduce the risk of post-surgical ectasia; age, refractive error before surgery, topography before surgery, corneal thickness, and residual stromal bed. 

Case Presentation

A 10-year-old middle eastern female is referred by her Primary Care Physician for decreased vision. She reported a mild decrease in vision over the last few years and was bothered by blur and shadowing. 

POH: S/p LASIK at 3 years old, strabismus surgery at 4 years old 

PMH: unremarkable 

Medications: no medications 

PFH: (+) postsurgical ectasia – father 

BCVA w/ spectacles: 20/25+2 OD; 20/25-2 OS* 

Preliminary Testing: normal EOMs; PERRL (-) APD; FTFC OU; CT ortho at distance and near 

Slit Lamp Evaluation: LASIK flaps in place; (-) haze, (-) scarring OU 

Ancillary Testing:  

Topography: (OD) Flat K 41.6D; Steep K 42.7D; HVID 12.0mm, (OS) Flat K 39.1D; Steep K 41.6D; HVID 12.1mm 

Pachymetry: (OD) 513um; (OS) 483um 

Based on this presentation, all differentials for these corneal irregularities must be considered, such as keratoconus, Terrien’s marginal degeneration, and pellucid marginal degeneration. However, given this patient’s history and age, it is appropriate to conclude that her corneal irregularities resulted from the procedure she underwent at a young age. 

* It is important to note that while vision is not measured to be remarkably reduced, irregularities on the cornea can produce higher order aberrations leading to decreased functionality of seemingly good vision, and given the age of the patient, the risk of progression is increased. 

Lens Fitting

Corneal gas permeable lenses were chosen to provide superior optics while also being a lower cost option and having simple insertion and removal technique. A topography scan provided further information on the best starting point for fitting these customized corneal gas permeable lenses. A large diameter corneal gas permeable lens was chosen for both eyes with the addition of reverse geometry technology for the left eye. 

When approaching a complicated fit as this case is, it is helpful to use all the tools available. At this teaching clinic, lenses from our fit set were placed on the eye at the initial visit to diagnostically determine which parameters needed to be changed. The first set of lenses ordered were designed based on the diagnostic fitting as well as the utilization of lens design software to better determine the degree of changes to be made.  

Fitting Set:  

(OD) BC: 8.04 || PWR:-0.62 || DIA:10.8 || EL: Standard 

Fit: mild central bearing, patient reported discomfort 

OR: -0.25sph  

VA: 20/20-2 

Plan: steepen lens and incorporate over refraction 

(OS) BC: 8.65 || PWR:-0.37 || DIA:10.8 || EL: Standard Series C 

Fit: too much edge lift, bearing centrally (Photo 1) 

OR: +0.25 

VA: 20/25-3 

Plan: increase reverse geometry and steepen BC 

 

Follow-up: 

(OD) BC: 7.89 || PWR:-1.62 || DIA:10.8 || EL: Standard  

Fit: good fit with adequate tear exchange and appropriate comfort. 

VA: 20/20 

OR: plano 

Plan:  no changes 

(OS) BC: 8.44  || PWR:-1.12 || DIA:10.8 || EL:1 Flat || SERIES E 

Fit: central bearing, thin edges 

VA: 20/20-3 

OR: -0.25sph 

Plan: increase reverse geometry, flatten edges (Figure 2) 

 

Final Dispense: 

Intralimbal GP- Optimum Extra Green 

(OD) BC:7.89 || PWR: -1.62 || DIA:10.8 || ET:0.14 || EL:Standard || 1 DOT 

VA: 20/20
   

Reverse Geometry GP- Optimum Extra Blue 

(OS) BC: 8.44 || PWR: -1.37 || DIA:10.8 || EL:3 Flat || SERIES F 

VA: 20/20-1 

Conclusion

When screening candidates for the LASIK procedure, it is important to consider the age, refractive error before surgery, topographic pattern before surgery, central corneal thickness, and residual stromal bed. All these factors pose a risk for post-surgical corneal ectasia. The age at which this patient received the LASIK procedure puts her at increased risk for not only corneal ectasia, but further changes in her refractive error alone. There are few studies published that have explored the long-term stability of LASIK in children this young.  

When fitting a custom specialty lens, it is important to consider the individual needs of the patient. This patient is at a visually demanding time of her life where decreased quality of vision may impact her education and other activities. This case demonstrates a successful fit of corneal gas permeable lenses that met the visual needs of the patient and relieved the shadowing and blur she reported at presentation. Patients with post-surgical irregularities should be closely monitored for further progression with repeat tomography. If further corneal changes are noted, the patient should be considered for corneal cross linking to halt the progression of postsurgical ectasia. 

References

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Author spotlight

Gillian Uldrich

Gillian Uldrich, OD graduated from Pennsylvania College of Optometry in 2024, with honors and a certificate for Advanced Studies in Contact Lenses. Dr. Uldrich will be going on to complete her residency in Cornea and Contact lenses at Indiana University. She has completed multiple workshops, presented at conferences, competed in academic challenges and is passionate about fitting specialty lenses and taking on challenging or unusual cases. While still early on in her career, she will be a name to look out for in the future of specialty contact lenses.  

Nicholas Gidosh

Nicholas Gidosh, OD is an associate professor at the Pennsylvania College of Optometry. Dr. Gidosh has extensive experience in the field of optometry, with a focus on cornea and contact lens services. He has presented lectures and workshops on topics including scleral and hybrid lenses, irregular cornea, myopia control, and orthokeratology. Dr. Gidosh is also a Fellow of the American Academy of Optometry and is involved in ongoing research on optimizing scleral lens designs for patients with irregular corneas and those with multifocal needs. Additionally, he researches and lectures on myopia control strategies, particularly orthokeratology for patients with astigmatism.